Mitochondrial succinate is instrumental for HIF1alpha nuclear translocation in SDHA-mutant fibroblasts under normoxic conditions. [electronic resource]
- Human molecular genetics Nov 2005
- 3263-9 p. digital
Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't
0964-6906
10.1093/hmg/ddi359 doi
Blotting, Western DNA Primers Fibroblasts Gas Chromatography-Mass Spectrometry Humans Hypoxia-Inducible Factor 1, alpha Subunit--metabolism Iron--metabolism Isoenzymes--metabolism Ketoglutaric Acids--metabolism Microscopy, Fluorescence Mitochondria--metabolism Mutation--genetics Protein Transport--physiology Succinate Dehydrogenase--genetics Succinic Acid--metabolism Superoxides--metabolism