Bridi, Raquel

alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats. [electronic resource] - Metabolic brain disease Jun 2005 - 155-67 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0885-7490

10.1007/s11011-005-4152-8 doi


Animals
Antioxidants--metabolism
Catalase--metabolism
Cerebral Cortex--chemistry
Disease Models, Animal
Free Radicals--metabolism
Glutathione Peroxidase--metabolism
Hemiterpenes
Keto Acids--metabolism
Lipid Peroxidation--drug effects
Male
Maple Syrup Urine Disease--metabolism
Oxidative Stress--physiology
Rats
Rats, Wistar
Superoxide Dismutase--metabolism
Thiobarbituric Acid Reactive Substances--metabolism