Monolysocardiolipins accumulate in Barth syndrome but do not lead to enhanced apoptosis. [electronic resource]
- Journal of lipid research Jun 2005
- 1182-95 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
0022-2275
10.1194/jlr.M500056-JLR200 doi
Acylation Apoptosis BH3 Interacting Domain Death Agonist Protein Cardiolipins--chemistry Cardiomyopathies--metabolism Carrier Proteins--metabolism Cell Death Chromatography, High Pressure Liquid Chromosomes, Human, X Cytochromes c--metabolism Genes, Recessive Genetic Linkage Growth Disorders--metabolism Humans Immunoblotting Jurkat Cells Lipid Metabolism Lymphocytes--metabolism Lysophospholipids--chemistry Mass Spectrometry Mitochondria--metabolism Muscles--metabolism Muscular Diseases--metabolism Myocardium--metabolism Phospholipids--metabolism Poly(ADP-ribose) Polymerases--metabolism Protein Structure, Tertiary Subcellular Fractions Syndrome fas Receptor--metabolism