A non-sequence-specific requirement for SMN protein activity: the role of aminoglycosides in inducing elevated SMN protein levels. [electronic resource]
- Human molecular genetics May 2005
- 1199-210 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
0964-6906
10.1093/hmg/ddi131 doi
Alanine--metabolism Amikacin--pharmacology Amino Acid Substitution Aminoglycosides--metabolism Anti-Bacterial Agents--pharmacology Antibodies, Monoclonal--metabolism Blotting, Western Cells, Cultured Codon, Terminator Cyclic AMP Response Element-Binding Protein--genetics Dose-Response Relationship, Drug Epithelial Cells--drug effects Exons Fibroblasts--drug effects Fluorescein-5-isothiocyanate Fluorescent Antibody Technique Fluorescent Dyes Gene Deletion HeLa Cells Homozygote Humans Immunohistochemistry Indoles Kinetics Muscular Atrophy, Spinal--genetics Nerve Tissue Proteins--deficiency RNA-Binding Proteins--genetics SMN Complex Proteins Survival of Motor Neuron 1 Protein Survival of Motor Neuron 2 Protein Tissue Distribution Tobramycin--pharmacology Transcription, Genetic