Wolstencroft, Elizabeth C

A non-sequence-specific requirement for SMN protein activity: the role of aminoglycosides in inducing elevated SMN protein levels. [electronic resource] - Human molecular genetics May 2005 - 1199-210 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0964-6906

10.1093/hmg/ddi131 doi


Alanine--metabolism
Amikacin--pharmacology
Amino Acid Substitution
Aminoglycosides--metabolism
Anti-Bacterial Agents--pharmacology
Antibodies, Monoclonal--metabolism
Blotting, Western
Cells, Cultured
Codon, Terminator
Cyclic AMP Response Element-Binding Protein--genetics
Dose-Response Relationship, Drug
Epithelial Cells--drug effects
Exons
Fibroblasts--drug effects
Fluorescein-5-isothiocyanate
Fluorescent Antibody Technique
Fluorescent Dyes
Gene Deletion
HeLa Cells
Homozygote
Humans
Immunohistochemistry
Indoles
Kinetics
Muscular Atrophy, Spinal--genetics
Nerve Tissue Proteins--deficiency
RNA-Binding Proteins--genetics
SMN Complex Proteins
Survival of Motor Neuron 1 Protein
Survival of Motor Neuron 2 Protein
Tissue Distribution
Tobramycin--pharmacology
Transcription, Genetic