Meng, Yan

Restoration of copper metabolism and rescue of hepatic abnormalities in LEC rats, an animal model of Wilson disease, by expression of human ATP7B gene. [electronic resource] - Biochimica et biophysica acta Nov 2004 - 208-19 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/j.bbadis.2004.06.022 doi


Adenosine Triphosphatases--genetics
Aging--physiology
Animals
Animals, Genetically Modified
Carcinoma, Hepatocellular--genetics
Cation Transport Proteins--genetics
Ceruloplasmin--biosynthesis
Copper--metabolism
Copper-Transporting ATPases
Disease Models, Animal
Female
Gene Expression
Hepatitis, Animal--genetics
Hepatolenticular Degeneration--genetics
Humans
Iron--metabolism
Liver--abnormalities
Rats
Rats, Inbred LEC
Rats, Sprague-Dawley
Survival Rate
Transgenes--genetics