Pacheco-Alvarez, Diana

Paradoxical regulation of biotin utilization in brain and liver and implications for inherited multiple carboxylase deficiency. [electronic resource] - The Journal of biological chemistry Dec 2004 - 52312-8 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0021-9258

10.1074/jbc.M407056200 doi


Animals
Base Sequence
Biotin--deficiency
Brain--metabolism
Carbon-Nitrogen Ligases--genetics
Cell Line
DNA, Complementary--genetics
Holocarboxylase Synthetase Deficiency--genetics
Humans
Liver--metabolism
Male
Multiple Carboxylase Deficiency--genetics
RNA, Messenger--genetics
Rats
Rats, Wistar
Tissue Distribution