Paradoxical regulation of biotin utilization in brain and liver and implications for inherited multiple carboxylase deficiency. [electronic resource]
- The Journal of biological chemistry Dec 2004
- 52312-8 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0021-9258
10.1074/jbc.M407056200 doi
Animals Base Sequence Biotin--deficiency Brain--metabolism Carbon-Nitrogen Ligases--genetics Cell Line DNA, Complementary--genetics Holocarboxylase Synthetase Deficiency--genetics Humans Liver--metabolism Male Multiple Carboxylase Deficiency--genetics RNA, Messenger--genetics Rats Rats, Wistar Tissue Distribution