TY - GEN AU - Pecina,Petr AU - Gnaiger,Erich AU - Zeman,JirĂ­ AU - Pronicka,Ewa AU - Houstek,Josef TI - Decreased affinity for oxygen of cytochrome-c oxidase in Leigh syndrome caused by SURF1 mutations SN - 0363-6143 PY - 2004///1110 KW - Cells, Cultured KW - Cytochrome-c Oxidase Deficiency KW - genetics KW - Electron Transport Complex IV KW - metabolism KW - Fibroblasts KW - Humans KW - Leigh Disease KW - Membrane Proteins KW - Mitochondrial Proteins KW - Mutation KW - Oxygen KW - Oxygen Consumption KW - physiology KW - Proteins N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1152/ajpcell.00286.2004 ER -