Severe ADAMTS13 deficiency in adult idiopathic thrombotic microangiopathies defines a subset of patients characterized by various autoimmune manifestations, lower platelet count, and mild renal involvement. [electronic resource]
- Medicine Jul 2004
- 233-244 p. digital
Publication Type: Journal Article; Multicenter Study; Research Support, Non-U.S. Gov't
0025-7974
10.1097/01.md.0000133622.03370.07 doi
ADAM Proteins ADAMTS13 Protein Adolescent Adult Aged Autoimmune Diseases--etiology Female Humans Kidney Diseases--etiology Male Metalloendopeptidases--deficiency Middle Aged Platelet Count Prognosis Retrospective Studies Severity of Illness Index Thrombocytopenia--etiology Thrombosis--etiology von Willebrand Factor