Coppo, Paul

Severe ADAMTS13 deficiency in adult idiopathic thrombotic microangiopathies defines a subset of patients characterized by various autoimmune manifestations, lower platelet count, and mild renal involvement. [electronic resource] - Medicine Jul 2004 - 233-244 p. digital

Publication Type: Journal Article; Multicenter Study; Research Support, Non-U.S. Gov't

0025-7974

10.1097/01.md.0000133622.03370.07 doi


ADAM Proteins
ADAMTS13 Protein
Adolescent
Adult
Aged
Autoimmune Diseases--etiology
Female
Humans
Kidney Diseases--etiology
Male
Metalloendopeptidases--deficiency
Middle Aged
Platelet Count
Prognosis
Retrospective Studies
Severity of Illness Index
Thrombocytopenia--etiology
Thrombosis--etiology
von Willebrand Factor