TY  - GEN
AU  - Kasinski,Andrea
AU  - Doering,Christopher B
AU  - Danner,Dean J
TI  - Leucine toxicity in a neuronal cell model with inhibited branched chain amino acid catabolism
SN  - 0169-328X
PY  - 2004///0712
KW  - 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)
KW  - deficiency
KW  - Animals
KW  - Apoptosis
KW  - genetics
KW  - Cell Survival
KW  - drug effects
KW  - Doxycycline
KW  - pharmacology
KW  - Leucine
KW  - metabolism
KW  - Maple Syrup Urine Disease
KW  - enzymology
KW  - Mitochondria
KW  - Models, Biological
KW  - Nerve Degeneration
KW  - Neurons
KW  - PC12 Cells
KW  - Proteins
KW  - RNA, Messenger
KW  - Rats
KW  - Reaction Time
KW  - Transgenes
N1  - Publication Type: Journal Article
UR  - https://doi.org/10.1016/j.molbrainres.2003.08.023
ER  -