Kasinski, Andrea

Leucine toxicity in a neuronal cell model with inhibited branched chain amino acid catabolism. [electronic resource] - Brain research. Molecular brain research Mar 2004 - 180-7 p. digital

Publication Type: Journal Article

0169-328X

10.1016/j.molbrainres.2003.08.023 doi


3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)--deficiency
Animals
Apoptosis--genetics
Cell Survival--drug effects
Doxycycline--pharmacology
Leucine--metabolism
Maple Syrup Urine Disease--enzymology
Mitochondria--drug effects
Models, Biological
Nerve Degeneration--enzymology
Neurons--drug effects
PC12 Cells
Proteins--metabolism
RNA, Messenger--drug effects
Rats
Reaction Time--drug effects
Transgenes--genetics