Kasinski, Andrea Leucine toxicity in a neuronal cell model with inhibited branched chain amino acid catabolism. [electronic resource] - Brain research. Molecular brain research Mar 2004 - 180-7 p. digital Publication Type: Journal Article ISSN: 0169-328X Standard No.: 10.1016/j.molbrainres.2003.08.023 doi Subjects--Topical Terms: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)--deficiencyAnimalsApoptosis--geneticsCell Survival--drug effectsDoxycycline--pharmacologyLeucine--metabolismMaple Syrup Urine Disease--enzymologyMitochondria--drug effectsModels, BiologicalNerve Degeneration--enzymologyNeurons--drug effectsPC12 CellsProteins--metabolismRNA, Messenger--drug effectsRatsReaction Time--drug effectsTransgenes--genetics