TY  - GEN
AU  - Simon,Delphine
AU  - Seznec,Hervé
AU  - Gansmuller,Anne
AU  - Carelle,Nadège
AU  - Weber,Philipp
AU  - Metzger,Daniel
AU  - Rustin,Pierre
AU  - Koenig,Michel
AU  - Puccio,Hélène
TI  - Friedreich ataxia mouse models with progressive cerebellar and sensory ataxia reveal autophagic neurodegeneration in dorsal root ganglia
SN  - 1529-2401
PY  - 2004///0430
KW  - Animals
KW  - Ataxia
KW  - etiology
KW  - Autophagy
KW  - genetics
KW  - Cerebellar Ataxia
KW  - Disease Models, Animal
KW  - Disease Progression
KW  - Friedreich Ataxia
KW  - complications
KW  - Ganglia, Spinal
KW  - pathology
KW  - Iron-Binding Proteins
KW  - Mice
KW  - Mice, Knockout
KW  - Mice, Neurologic Mutants
KW  - Motor Activity
KW  - Nerve Degeneration
KW  - Phenotype
KW  - Sensation Disorders
KW  - Frataxin
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1523/JNEUROSCI.4549-03.2004
ER  -