TY  - GEN
AU  - Russell,Aaron P
AU  - Schrauwen,Patrick
AU  - Somm,Emmanuel
AU  - Gastaldi,Giacomo
AU  - Hesselink,Matthijs K C
AU  - Schaart,Gert
AU  - Kornips,Esther
AU  - Lo,Sing Kai
AU  - Bufano,Daniela
AU  - Giacobino,Jean-Paul
AU  - Muzzin,Patrick
AU  - Ceccon,Mara
AU  - Angelini,Corrado
AU  - Vergani,Lodovica
TI  - Decreased fatty acid beta-oxidation in riboflavin-responsive, multiple acylcoenzyme A dehydrogenase-deficient patients is associated with an increase in uncoupling protein-3
SN  - 0021-972X
PY  - 2004///0115
KW  - Acyl-CoA Dehydrogenase
KW  - deficiency
KW  - Adolescent
KW  - Adult
KW  - Carrier Proteins
KW  - genetics
KW  - Cohort Studies
KW  - Electron Transport Complex I
KW  - Electron Transport Complex II
KW  - Fatty Acids
KW  - metabolism
KW  - Female
KW  - Humans
KW  - Ion Channels
KW  - Lipid Metabolism
KW  - Male
KW  - Middle Aged
KW  - Mitochondrial Proteins
KW  - Muscle, Skeletal
KW  - enzymology
KW  - Oxidation-Reduction
KW  - RNA, Messenger
KW  - Riboflavin
KW  - therapeutic use
KW  - Uncoupling Protein 3
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1210/jc.2003-030885
ER  -