TY - GEN AU - Joseph,Anna-Maria AU - Rungi,Arne A AU - Robinson,Brian H AU - Hood,David A TI - Compensatory responses of protein import and transcription factor expression in mitochondrial DNA defects SN - 0363-6143 PY - 2004///0420 KW - Animals KW - Carrier Proteins KW - genetics KW - DNA, Mitochondrial KW - DNA-Binding Proteins KW - Fibroblasts KW - cytology KW - Gene Expression KW - High Mobility Group Proteins KW - MELAS Syndrome KW - metabolism KW - Membrane Potentials KW - physiology KW - Membrane Transport Proteins KW - Mice KW - Mitochondrial Membrane Transport Proteins KW - Mitochondrial Precursor Protein Import Complex Proteins KW - Mitochondrial Proteins KW - Muscle Contraction KW - Muscle, Skeletal KW - Myoblasts, Skeletal KW - NF-E2-Related Factor 1 KW - Nuclear Proteins KW - Nuclear Respiratory Factor 1 KW - Nuclear Respiratory Factors KW - Prostaglandin-Endoperoxide Synthases KW - Protein Transport KW - Receptors, Cell Surface KW - Trans-Activators KW - Transcription Factors KW - Xenopus Proteins N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1152/ajpcell.00191.2003 ER -