Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain. [electronic resource]
- The Journal of biological chemistry Nov 2003
- 47388-93 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0021-9258
10.1074/jbc.M308861200 doi
Acyl Coenzyme A--metabolism Adenosine Triphosphate--metabolism Aging Amino Acid Metabolism, Inborn Errors--metabolism Animals Cattle Citrates--metabolism Citric Acid Cycle Dose-Response Relationship, Drug Electron Transport Female Hydrogen-Ion Concentration Male Malonates--metabolism Methylmalonic Acid--chemistry Mice Mice, Inbred C57BL Mitochondria--metabolism Mitochondrial Diseases--metabolism Muscles--metabolism Myocardium--metabolism Oxygen--metabolism Phosphorylation Pyruvates--metabolism Spectrophotometry Time Factors