RNA-mediated neurodegeneration caused by the fragile X premutation rCGG repeats in Drosophila. [electronic resource]
- Neuron Aug 2003
- 739-47 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
0896-6273
10.1016/s0896-6273(03)00533-6 doi
Animals Blotting, Western Disease Models, Animal Drosophila Eye--pathology Female Fluorescent Antibody Technique Fragile X Mental Retardation Protein Fragile X Syndrome--genetics HSP70 Heat-Shock Proteins--metabolism Humans Inclusion Bodies--metabolism Male Microscopy, Electron Mutation Nerve Degeneration--genetics Nerve Tissue Proteins--genetics Neurons--metabolism RNA, Messenger--analysis RNA-Binding Proteins Reverse Transcriptase Polymerase Chain Reaction Transgenes Trinucleotide Repeat Expansion--genetics Ubiquitin--metabolism