Intestinal Wegener's granulomatosis in a patient with severe alpha-1-antitrypsin deficiency resulting from a unique combination of two deficiency alleles (PiZ and PiMProcida). [electronic resource]
- European journal of gastroenterology & hepatology Dec 2002
- 1389-92 p. digital
Publication Type: Case Reports; Journal Article
0954-691X
10.1097/00042737-200212000-00017 doi
Colitis--complications Crohn Disease--complications Granulomatosis with Polyangiitis--complications Heterozygote Humans Ileitis--complications Male Middle Aged Mutation--genetics Pulmonary Emphysema--complications alpha 1-Antitrypsin Deficiency--complications