Lonardo, Amedeo

Intestinal Wegener's granulomatosis in a patient with severe alpha-1-antitrypsin deficiency resulting from a unique combination of two deficiency alleles (PiZ and PiMProcida). [electronic resource] - European journal of gastroenterology & hepatology Dec 2002 - 1389-92 p. digital

Publication Type: Case Reports; Journal Article

0954-691X

10.1097/00042737-200212000-00017 doi


Colitis--complications
Crohn Disease--complications
Granulomatosis with Polyangiitis--complications
Heterozygote
Humans
Ileitis--complications
Male
Middle Aged
Mutation--genetics
Pulmonary Emphysema--complications
alpha 1-Antitrypsin Deficiency--complications