Carrell, Robin W

Alpha1-antitrypsin deficiency--a model for conformational diseases. [electronic resource] - The New England journal of medicine Jan 2002 - 45-53 p. digital

Publication Type: Journal Article; Review

0028-4793

10.1056/NEJMra010772 doi


Dementia--etiology
Emphysema--etiology
Endopeptidases--metabolism
Humans
Liver Cirrhosis--etiology
Models, Biological
Mutation
Neurodegenerative Diseases--etiology
Protease Inhibitors--metabolism
Protein Conformation
Serpins--chemistry
alpha 1-Antitrypsin--chemistry
alpha 1-Antitrypsin Deficiency--metabolism