TY - GEN AU - Vielhaber,S AU - Schröder,R AU - Winkler,K AU - Weis,S AU - Sailer,M AU - Feistner,H AU - Heinze,H J AU - Schröder,J M AU - Kunz,W S TI - Defective mitochondrial oxidative phosphorylation in myopathies with tubular aggregates originating from sarcoplasmic reticulum SN - 0022-3069 PY - 2001///1207 KW - Adult KW - Biopsy KW - Calcium-Transporting ATPases KW - analysis KW - Calsequestrin KW - Cell Respiration KW - DNA, Mitochondrial KW - Energy Metabolism KW - Humans KW - Immunohistochemistry KW - Male KW - Microscopy, Electron KW - Middle Aged KW - Mitochondrial Myopathies KW - metabolism KW - Muscle Fibers, Skeletal KW - chemistry KW - Muscle, Skeletal KW - Oxidative Phosphorylation KW - Ryanodine Receptor Calcium Release Channel KW - Saponins KW - Sarcoplasmic Reticulum KW - Sarcoplasmic Reticulum Calcium-Transporting ATPases KW - Titrimetry N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1093/jnen/60.11.1032 ER -