Vielhaber, S

Defective mitochondrial oxidative phosphorylation in myopathies with tubular aggregates originating from sarcoplasmic reticulum. [electronic resource] - Journal of neuropathology and experimental neurology Nov 2001 - 1032-40 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0022-3069

10.1093/jnen/60.11.1032 doi


Adult
Biopsy
Calcium-Transporting ATPases--analysis
Calsequestrin--analysis
Cell Respiration
DNA, Mitochondrial--analysis
Energy Metabolism
Humans
Immunohistochemistry
Male
Microscopy, Electron
Middle Aged
Mitochondrial Myopathies--metabolism
Muscle Fibers, Skeletal--chemistry
Muscle, Skeletal--chemistry
Oxidative Phosphorylation
Ryanodine Receptor Calcium Release Channel--analysis
Saponins
Sarcoplasmic Reticulum--metabolism
Sarcoplasmic Reticulum Calcium-Transporting ATPases
Titrimetry