Waelter, S
Accumulation of mutant huntingtin fragments in aggresome-like inclusion bodies as a result of insufficient protein degradation. [electronic resource]
- Molecular biology of the cell May 2001
- 1393-407 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
ISSN: 1059-1524
Standard No.: 10.1091/mbc.12.5.1393 doi
Subjects--Topical Terms: 14-3-3 Proteins Acetylcysteine--analogs & derivatives Carrier Proteins--metabolism Cell Line Cysteine Endopeptidases--metabolism Cysteine Proteinase Inhibitors--pharmacology Endoplasmic Reticulum Chaperone BiP Exons Heat-Shock Proteins Humans Huntingtin Protein Huntington Disease--metabolism Immunoblotting Inclusion Bodies--metabolism Membrane Proteins--metabolism Microscopy, Fluorescence Models, Biological Molecular Chaperones--metabolism Multienzyme Complexes--antagonists & inhibitors Mutation Nerve Tissue Proteins--genetics Nuclear Proteins--genetics Peptide Fragments--genetics Poly(A)-Binding Proteins Proteasome Endopeptidase Complex Proteins RNA-Binding Proteins--metabolism Recombinant Fusion Proteins--genetics Synucleins T-Cell Intracellular Antigen-1 Transgenes Tyrosine 3-Monooxygenase--metabolism Vimentin--metabolism alpha-Synuclein