Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice. [electronic resource]
- The Journal of cell biology Mar 2001
- 1207-18 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
0021-9525
10.1083/jcb.152.6.1207 doi
Animals Blotting, Western Body Weight Contracture--physiopathology Creatine Kinase--genetics Creatine Kinase, MM Form Cytoskeletal Proteins--genetics Dystrophin--genetics Female Hindlimb Humans Integrins--genetics Isoenzymes--genetics Joints Kyphosis Magnetic Resonance Imaging Male Membrane Proteins--genetics Mice Mice, Inbred mdx Mice, Transgenic Microscopy, Fluorescence Muscle, Skeletal--pathology Muscular Dystrophy, Animal--genetics Muscular Dystrophy, Duchenne--genetics Neuromuscular Junction--ultrastructure Promoter Regions, Genetic Rats Receptors, Cholinergic--metabolism Survival Rate Transgenes Utrophin