TY  - GEN
AU  - Harada,M
AU  - Sakisaka,S
AU  - Terada,K
AU  - Kimura,R
AU  - Kawaguchi,T
AU  - Koga,H
AU  - Kim,M
AU  - Taniguchi,E
AU  - Hanada,S
AU  - Suganuma,T
AU  - Furuta,K
AU  - Sugiyama,T
AU  - Sata,M
TI  - A mutation of the Wilson disease protein, ATP7B, is degraded in the proteasomes and forms protein aggregates
SN  - 0016-5085
PY  - 2001///0419
KW  - Acetylcysteine
KW  - analogs & derivatives
KW  - Adenosine Triphosphatases
KW  - genetics
KW  - Carrier Proteins
KW  - Cation Transport Proteins
KW  - Cell Line
KW  - Copper-Transporting ATPases
KW  - Cysteine Endopeptidases
KW  - drug effects
KW  - Cytoskeleton
KW  - ultrastructure
KW  - Fluorescent Antibody Technique
KW  - Humans
KW  - Leupeptins
KW  - pharmacology
KW  - Microscopy, Confocal
KW  - Microscopy, Electron
KW  - Multienzyme Complexes
KW  - Mutation
KW  - physiology
KW  - Proteasome Endopeptidase Complex
KW  - Tissue Distribution
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1053/gast.2001.22543
ER  -