Harada, M

A mutation of the Wilson disease protein, ATP7B, is degraded in the proteasomes and forms protein aggregates. [electronic resource] - Gastroenterology Mar 2001 - 967-74 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0016-5085

10.1053/gast.2001.22543 doi


Acetylcysteine--analogs & derivatives
Adenosine Triphosphatases--genetics
Carrier Proteins--genetics
Cation Transport Proteins
Cell Line
Copper-Transporting ATPases
Cysteine Endopeptidases--drug effects
Cytoskeleton--ultrastructure
Fluorescent Antibody Technique
Humans
Leupeptins--pharmacology
Microscopy, Confocal
Microscopy, Electron
Multienzyme Complexes--drug effects
Mutation--physiology
Proteasome Endopeptidase Complex
Tissue Distribution