TY - GEN AU - Vorgerd,M AU - Schöls,L AU - Hardt,C AU - Ristow,M AU - Epplen,J T AU - Zange,J TI - Mitochondrial impairment of human muscle in Friedreich ataxia in vivo SN - 0960-8966 PY - 2000///0915 KW - Adenosine Triphosphate KW - biosynthesis KW - Adolescent KW - Adult KW - Age Factors KW - Alleles KW - Exercise Test KW - Female KW - Friedreich Ataxia KW - genetics KW - Humans KW - Iron-Binding Proteins KW - Isometric Contraction KW - Magnetic Resonance Spectroscopy KW - Male KW - Middle Aged KW - Mitochondria, Muscle KW - metabolism KW - Muscle, Skeletal KW - Muscular Dystrophy, Duchenne KW - Phosphocreatine KW - Phosphorus Isotopes KW - analysis KW - Phosphotransferases (Alcohol Group Acceptor) KW - Trinucleotide Repeats KW - Frataxin N1 - Publication Type: Clinical Trial; Controlled Clinical Trial; Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1016/s0960-8966(00)00108-5 ER -