Effect of idebenone on cardiomyopathy in Friedreich's ataxia: a preliminary study. [electronic resource]
- Lancet (London, England) Aug 1999
- 477-9 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0140-6736
10.1016/S0140-6736(99)01341-0 doi
Adult Antioxidants--adverse effects Benzoquinones--adverse effects Cardiac Volume--drug effects Cardiomyopathies--drug therapy Child Electron Transport Complex II Female Friedreich Ataxia--drug therapy Humans Iron Chelating Agents--adverse effects Male Multienzyme Complexes--metabolism Myocardium--pathology Oxidoreductases--metabolism Succinate Dehydrogenase--metabolism Ubiquinone--analogs & derivatives