TY - GEN AU - Shimozawa,N AU - Zhang,Z AU - Suzuki,Y AU - Imamura,A AU - Tsukamoto,T AU - Osumi,T AU - Fujiki,Y AU - Orii,T AU - Barth,P G AU - Wanders,R J AU - Kondo,N TI - Functional heterogeneity of C-terminal peroxisome targeting signal 1 in PEX5-defective patients SN - 0006-291X PY - 1999///1001 KW - 17-Hydroxysteroid Dehydrogenases KW - 3-Hydroxyacyl CoA Dehydrogenases KW - metabolism KW - Acyl-CoA Oxidase KW - Biological Transport KW - Carrier Proteins KW - Cell Compartmentation KW - Enoyl-CoA Hydratase KW - Fibroblasts KW - cytology KW - Humans KW - Hydro-Lyases KW - Microbodies KW - Multienzyme Complexes KW - Mutation KW - Oxidoreductases KW - Peroxisomal Disorders KW - genetics KW - Peroxisomal Multifunctional Protein-2 KW - Peroxisomal Targeting Signal 2 Receptor KW - Peroxisome-Targeting Signal 1 Receptor KW - Protein Sorting Signals KW - Receptors, Cytoplasmic and Nuclear KW - Sterols KW - Transformation, Genetic KW - Zellweger Syndrome N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1006/bbrc.1999.1232 ER -