Shimozawa, N

Functional heterogeneity of C-terminal peroxisome targeting signal 1 in PEX5-defective patients. [electronic resource] - Biochemical and biophysical research communications Aug 1999 - 504-8 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-291X

10.1006/bbrc.1999.1232 doi


17-Hydroxysteroid Dehydrogenases
3-Hydroxyacyl CoA Dehydrogenases--metabolism
Acyl-CoA Oxidase
Biological Transport
Carrier Proteins--metabolism
Cell Compartmentation
Enoyl-CoA Hydratase
Fibroblasts--cytology
Humans
Hydro-Lyases--metabolism
Microbodies--metabolism
Multienzyme Complexes--metabolism
Mutation
Oxidoreductases--metabolism
Peroxisomal Disorders--genetics
Peroxisomal Multifunctional Protein-2
Peroxisomal Targeting Signal 2 Receptor
Peroxisome-Targeting Signal 1 Receptor
Protein Sorting Signals--genetics
Receptors, Cytoplasmic and Nuclear--genetics
Sterols
Transformation, Genetic
Zellweger Syndrome--genetics