TY - GEN AU - Thomas,S R AU - Jaffe,A AU - Geddes,D M AU - Hodson,M E AU - Alton,E W TI - Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion SN - 0140-6736 PY - 1999///0907 KW - Adenosine Triphosphate KW - pharmacology KW - Adult KW - Amiloride KW - Bronchodilator Agents KW - Chloride Channels KW - drug effects KW - Chlorides KW - metabolism KW - Cystic Fibrosis KW - genetics KW - Cystic Fibrosis Transmembrane Conductance Regulator KW - Diuretics KW - Female KW - Forced Expiratory Volume KW - Homozygote KW - Humans KW - Isoproterenol KW - Male KW - Membrane Potentials KW - Mutation KW - Retrospective Studies N1 - Publication Type: Letter UR - https://doi.org/10.1016/S0140-6736(98)05447-6 ER -