Quinone analogs prevent enzymes targeted in Friedreich ataxia from iron-induced injury in vitro. [electronic resource]
- BioFactors (Oxford, England) 1999
- 247-51 p. digital
Publication Type: Journal Article
0951-6433
10.1002/biof.5520090220 doi
Aconitate Hydratase--drug effects Benzoquinones--pharmacology Coenzymes Deferoxamine--pharmacology Electron Transport Complex II Friedreich Ataxia--enzymology Humans Iron--antagonists & inhibitors Iron-Sulfur Proteins--deficiency Multienzyme Complexes--drug effects Oxidoreductases--drug effects Quinones--pharmacology Succinate Dehydrogenase--drug effects Ubiquinone--analogs & derivatives