Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia. [electronic resource]
Producer: 19971114Description: 215-7 p. digitalISSN:- 1061-4036
- Aconitate Hydratase -- deficiency
- Citric Acid Cycle
- Electron Transport
- Endocardium -- metabolism
- Friedreich Ataxia -- genetics
- Genes, Fungal
- Humans
- Iron -- metabolism
- Iron-Binding Proteins
- Iron-Sulfur Proteins -- deficiency
- Mitochondria -- metabolism
- Models, Biological
- Mutation
- Myocardium -- metabolism
- Oxidative Stress
- Phosphotransferases (Alcohol Group Acceptor) -- genetics
- Saccharomyces cerevisiae -- genetics
- Frataxin
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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