Application of inhibitor titrations for the detection of oxidative phosphorylation defects in saponin-skinned muscle fibers of patients with mitochondrial diseases. [electronic resource]
Producer: 19970519Description: 142-50 p. digitalISSN:- 0006-3002
- Adult
- Azides -- pharmacology
- Biopsy
- Electron Transport Complex I
- Enzyme Inhibitors -- pharmacology
- Female
- Humans
- In Vitro Techniques
- Male
- Mitochondrial Myopathies -- diagnosis
- NADH, NADPH Oxidoreductases -- metabolism
- Oligomycins -- pharmacology
- Oxidative Phosphorylation -- drug effects
- Oxygen Consumption -- drug effects
- Proton-Translocating ATPases -- antagonists & inhibitors
- Rotenone -- pharmacology
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Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't
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