Glycoprotein catabolism in brain tissue in the lysosomal enzyme deficiency diseases. [electronic resource]
Producer: 19760823Description: 31-48 p. digitalISSN:- 0065-2598
- Adolescent
- Binding Sites
- Brain -- metabolism
- Child
- Concanavalin A -- metabolism
- Fucose -- analysis
- Galactose -- analysis
- Gangliosidoses -- metabolism
- Gaucher Disease -- metabolism
- Glycoproteins -- metabolism
- Hexosamines -- analysis
- Humans
- Infant, Newborn
- Leukodystrophy, Globoid Cell -- metabolism
- Leukodystrophy, Metachromatic -- metabolism
- Lipidoses -- metabolism
- Lysosomes -- enzymology
- Mannose -- analysis
- Middle Aged
- Protein Binding
- Sialic Acids -- analysis
- Sphingolipidoses -- metabolism
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Publication Type: Journal Article; Review
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