Effect of glycosaminoglycans accumulation on the non-oxidative sulfur metabolism in mouse model of Sanfilippo syndrome, type B. [electronic resource]
Producer: 20200518Description: 567-576 p. digitalISSN:- 1734-154X
- Animals
- Cystathionine gamma-Lyase -- genetics
- Disease Models, Animal
- Glycosaminoglycans -- metabolism
- Heparitin Sulfate -- metabolism
- Humans
- Kidney -- metabolism
- Liver -- metabolism
- Mice
- Mucopolysaccharidosis III -- genetics
- Myocardium -- metabolism
- Oxidative Stress -- genetics
- Spleen -- metabolism
- Sulfur -- metabolism
- Sulfurtransferases -- genetics
- Thiosulfate Sulfurtransferase -- genetics
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Publication Type: Journal Article
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