Cathepsin B inhibition attenuates cardiovascular pathology in mucopolysaccharidosis I mice. [electronic resource]
Producer: 20180226Description: 102-109 p. digitalISSN:- 1879-0631
- Animals
- Aorta -- pathology
- Cardiovascular System -- diagnostic imaging
- Cathepsin B -- antagonists & inhibitors
- Collagenases -- metabolism
- Cysteine Proteinase Inhibitors -- therapeutic use
- Dipeptides -- therapeutic use
- Female
- Fibroblasts -- metabolism
- Heart Function Tests
- Heart Valve Diseases -- diagnostic imaging
- Humans
- Lysosomes -- metabolism
- Male
- Mice
- Mice, Inbred C57BL
- Mucopolysaccharidosis I -- diagnostic imaging
- Pancreatic Elastase -- metabolism
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Publication Type: Journal Article
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