Bone demineralization is improved by ivacaftor in patients with cystic fibrosis carrying the p.Gly551Asp mutation. [electronic resource]
Producer: 20180104Description: e67-e69 p. digitalISSN:- 1873-5010
- Adult
- Aminophenols -- administration & dosage
- Bone Demineralization, Pathologic -- etiology
- Bone Density -- drug effects
- Cells, Cultured
- Chloride Channel Agonists -- administration & dosage
- Cystic Fibrosis -- complications
- Cystic Fibrosis Transmembrane Conductance Regulator -- genetics
- Female
- Humans
- Male
- Middle Aged
- Mutation
- Osteoblasts -- drug effects
- Quinolones -- administration & dosage
- Statistics as Topic
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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