Determination of [U-13C]glucose turnover into various metabolite pools for the differential diagnosis of lactic acidemias. [electronic resource]
Producer: 19890803Description: 382-9 p. digitalISSN:- 0003-2697
- Amino Acids -- analysis
- Carbon Isotopes
- Cells, Cultured
- Cytochrome-c Oxidase Deficiency
- Diagnosis, Differential
- Electron Transport Complex IV -- analysis
- Fibroblasts -- metabolism
- Glucose -- metabolism
- Humans
- Infant
- Lactates -- blood
- Pyruvate Dehydrogenase Complex Deficiency Disease -- diagnosis
- Pyruvate Metabolism, Inborn Errors -- diagnosis
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Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
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