A novel human R25C-phospholamban mutation is associated with super-inhibition of calcium cycling and ventricular arrhythmia. [electronic resource]
Producer: 20160524Description: 164-74 p. digitalISSN:- 1755-3245
- Aged
- Animals
- Arrhythmias, Cardiac -- etiology
- Calcium -- metabolism
- Calcium-Binding Proteins -- genetics
- Cardiomyopathy, Dilated -- genetics
- Cells, Cultured
- Cyclic AMP-Dependent Protein Kinases -- metabolism
- HEK293 Cells
- Humans
- Isoproterenol -- pharmacology
- Male
- Middle Aged
- Mutation
- Myocytes, Cardiac -- metabolism
- Rats
- Ryanodine Receptor Calcium Release Channel -- metabolism
- Sarcoplasmic Reticulum -- metabolism
- Sarcoplasmic Reticulum Calcium-Transporting ATPases -- metabolism
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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