Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model. [electronic resource]
Producer: 20150323Description: 336-55 p. digitalISSN:- 1460-2156
- Acetyltransferases -- deficiency
- Animals
- Behavior, Animal
- Energy Metabolism -- physiology
- Gangliosides -- metabolism
- Glycosaminoglycans -- metabolism
- Mice
- Mice, Inbred C57BL
- Microtubule-Associated Proteins -- metabolism
- Mitochondrial Diseases -- etiology
- Mucopolysaccharidosis III -- complications
- Neuritis -- etiology
- Neurodegenerative Diseases -- etiology
- Neurologic Examination
- Proteostasis Deficiencies -- pathology
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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