Cystic fibrosis transmembrane conductance regulator (CFTR) potentiators protect G551D but not ΔF508 CFTR from thermal instability. [electronic resource]
Producer: 20141121Description: 5613-8 p. digitalISSN:- 1520-4995
- Amino Acid Substitution
- Aminophenols -- pharmacology
- Animals
- Cystic Fibrosis -- drug therapy
- Cystic Fibrosis Transmembrane Conductance Regulator -- agonists
- Female
- Humans
- Mutagenesis, Site-Directed
- Mutant Proteins -- agonists
- Oocytes -- metabolism
- Protein Stability -- drug effects
- Quinolones -- pharmacology
- Recombinant Proteins -- chemistry
- Temperature
- Xenopus laevis
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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