Proteostasis: bad news and good news from the endoplasmic reticulum. [electronic resource]
Producer: 20150511Description: w14001 p. digitalISSN:- 1424-3997
- Activating Transcription Factor 6 -- metabolism
- Cystic Fibrosis -- genetics
- Endoplasmic Reticulum -- metabolism
- Endoplasmic Reticulum Stress
- Endoribonucleases -- metabolism
- Enzyme Replacement Therapy
- Eukaryotic Initiation Factor-2 -- metabolism
- Hemophilia A -- genetics
- Humans
- Lysosomal Storage Diseases, Nervous System -- genetics
- Molecular Chaperones -- therapeutic use
- Neurodegenerative Diseases -- genetics
- Protein Folding
- Protein Serine-Threonine Kinases -- metabolism
- Proteostasis Deficiencies -- genetics
- Signal Transduction
- Unfolded Protein Response -- drug effects
- eIF-2 Kinase -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review
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