CLP1 links tRNA metabolism to progressive motor-neuron loss. [electronic resource]
Producer: 20130423Description: 474-80 p. digitalISSN:- 1476-4687
- Amyotrophic Lateral Sclerosis
- Animals
- Animals, Newborn
- Axons -- metabolism
- Cell Death
- Diaphragm -- innervation
- Embryo Loss
- Embryo, Mammalian -- metabolism
- Exons -- genetics
- Female
- Fibroblasts
- Male
- Mice
- Mice, Inbred C57BL
- Mice, Knockout
- Mice, Transgenic
- Motor Neurons -- metabolism
- Muscular Atrophy, Spinal
- Neuromuscular Diseases -- metabolism
- Oxidative Stress
- RNA Processing, Post-Transcriptional
- RNA, Transfer, Tyr -- genetics
- RNA-Binding Proteins
- Respiration
- Spinal Nerves -- cytology
- Transcription Factors -- deficiency
- Tumor Suppressor Protein p53 -- metabolism
- Tyrosine -- genetics
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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