PGC-1α rescues Huntington's disease proteotoxicity by preventing oxidative stress and promoting TFEB function. [electronic resource]
Producer: 20130131Description: 142ra97 p. digitalISSN:- 1946-6242
- Animals
- Basic Helix-Loop-Helix Leucine Zipper Transcription Factors -- genetics
- Huntington Disease -- complications
- Mice
- Mice, Transgenic
- Mitochondria -- drug effects
- Nerve Degeneration -- complications
- Oxidative Stress -- drug effects
- Peptides -- toxicity
- Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha
- Phenotype
- Protein Structure, Quaternary
- Reactive Oxygen Species -- metabolism
- Trans-Activators -- metabolism
- Transcription Factors
- Transcriptional Activation -- genetics
- Trinucleotide Repeat Expansion -- genetics
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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