Sporadic inclusion-body myositis: conformational multifactorial ageing-related degenerative muscle disease associated with proteasomal and lysosomal inhibition, endoplasmic reticulum stress, and accumulation of amyloid-β42 oligomers and phosphorylated tau. [electronic resource]
Producer: 20110615Description: e219-35 p. digitalISSN:- 2213-0276
- Age Factors
- Amyloid beta-Peptides -- metabolism
- Autophagy -- physiology
- Biopsy
- Endoplasmic Reticulum -- pathology
- Humans
- Lysosomes -- metabolism
- Microscopy, Electron
- Muscle Fibers, Skeletal -- pathology
- Muscles -- pathology
- Myositis, Inclusion Body -- pathology
- Myostatin -- metabolism
- Peptide Fragments -- metabolism
- Phosphorylation
- Proteasome Endopeptidase Complex -- metabolism
- Protein Conformation
- Proteostasis Deficiencies -- pathology
- Sirtuin 1 -- metabolism
- Ubiquitin-Protein Ligases -- metabolism
- alpha-Synuclein -- metabolism
- tau Proteins -- metabolism
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review
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