Disruption of mitochondrial homeostasis in organic acidurias: insights from human and animal studies. [electronic resource]
Producer: 20110624Description: 31-8 p. digitalISSN:- 1573-6881
- Acetyl-CoA C-Acyltransferase -- deficiency
- Adenosine Triphosphate -- metabolism
- Amino Acid Metabolism, Inborn Errors -- physiopathology
- Animals
- Barth Syndrome -- physiopathology
- Brain Diseases, Metabolic -- physiopathology
- Brain Diseases, Metabolic, Inborn -- physiopathology
- Carboxylic Acids -- metabolism
- Glutaryl-CoA Dehydrogenase -- deficiency
- Homeostasis -- physiology
- Humans
- Metabolism, Inborn Errors -- physiopathology
- Mitochondria -- metabolism
- Mitochondrial Diseases -- physiopathology
- Propionic Acidemia -- physiopathology
- Purpura -- physiopathology
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review
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