Stoichiometry of base excision repair proteins correlates with increased somatic CAG instability in striatum over cerebellum in Huntington's disease transgenic mice. [electronic resource]
Producer: 20100503Description: e1000749 p. digitalISSN:- 1553-7404
- Aging -- metabolism
- Animals
- Base Sequence
- Cerebellum -- enzymology
- DNA -- chemistry
- DNA Damage
- DNA Glycosylases -- metabolism
- DNA Polymerase beta -- metabolism
- DNA Repair -- genetics
- DNA Repair Enzymes -- genetics
- DNA-(Apurinic or Apyrimidinic Site) Lyase -- metabolism
- Flap Endonucleases -- metabolism
- Genomic Instability -- genetics
- Huntington Disease -- genetics
- Mice
- Mice, Transgenic
- Models, Genetic
- Molecular Sequence Data
- Neostriatum -- enzymology
- Nucleic Acid Conformation
- Organ Specificity -- genetics
- Substrate Specificity
- Trinucleotide Repeat Expansion -- genetics
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, N.I.H., Intramural; Research Support, Non-U.S. Gov't
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