Neuronal and glial accumulation of alpha- and beta-synucleins in human lipidoses. [electronic resource]
Producer: 20080219Description: 481-9 p. digitalISSN:- 0001-6322
- Adult
- Antigens, Nuclear -- metabolism
- Brain -- metabolism
- Brain Diseases, Metabolic, Inborn -- metabolism
- Child, Preschool
- Cohort Studies
- Humans
- Lipid Metabolism -- genetics
- Lipidoses -- metabolism
- Lysosomal Storage Diseases, Nervous System -- metabolism
- Male
- Middle Aged
- Nerve Tissue Proteins -- metabolism
- Neuroglia -- metabolism
- Neurons -- metabolism
- Peroxisomal Disorders -- metabolism
- Sandhoff Disease -- metabolism
- Synucleins -- analysis
- alpha-Synuclein -- metabolism
- beta-Synuclein -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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