Depletion of reduced glutathione enhances motor neuron degeneration in vitro and in vivo. [electronic resource]
Producer: 20070411Description: 991-1003 p. digitalISSN:- 0306-4522
- Amyotrophic Lateral Sclerosis -- metabolism
- Animals
- Apoptosis -- drug effects
- Apoptosis Inducing Factor -- drug effects
- Biomarkers -- metabolism
- Buthionine Sulfoximine -- toxicity
- Cell Line
- Down-Regulation -- drug effects
- Enzyme Inhibitors -- pharmacology
- Ethacrynic Acid -- toxicity
- Glutathione -- deficiency
- Mice
- Mice, Transgenic
- Motor Neurons -- metabolism
- Mutation -- genetics
- Nerve Degeneration -- metabolism
- Oxidative Stress -- physiology
- Reactive Oxygen Species -- metabolism
- Spinal Cord -- metabolism
- Superoxide Dismutase -- genetics
- Superoxide Dismutase-1
- Transcriptional Activation -- drug effects
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Publication Type: Journal Article; Research Support, N.I.H., Extramural
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