Monolysocardiolipins accumulate in Barth syndrome but do not lead to enhanced apoptosis. [electronic resource]
Producer: 20050922Description: 1182-95 p. digitalISSN:- 0022-2275
- Acylation
- Apoptosis
- BH3 Interacting Domain Death Agonist Protein
- Cardiolipins -- chemistry
- Cardiomyopathies -- metabolism
- Carrier Proteins -- metabolism
- Cell Death
- Chromatography, High Pressure Liquid
- Chromosomes, Human, X
- Cytochromes c -- metabolism
- Genes, Recessive
- Genetic Linkage
- Growth Disorders -- metabolism
- Humans
- Immunoblotting
- Jurkat Cells
- Lipid Metabolism
- Lymphocytes -- metabolism
- Lysophospholipids -- chemistry
- Mass Spectrometry
- Mitochondria -- metabolism
- Muscles -- metabolism
- Muscular Diseases -- metabolism
- Myocardium -- metabolism
- Phospholipids -- metabolism
- Poly(ADP-ribose) Polymerases -- metabolism
- Protein Structure, Tertiary
- Subcellular Fractions
- Syndrome
- fas Receptor -- metabolism
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
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