Hippocampal pathology in the human neuronal ceroid-lipofuscinoses: distinct patterns of storage deposition, neurodegeneration and glial activation. [electronic resource]
Producer: 20050214Description: 349-57 p. digitalISSN:- 1015-6305
- Adolescent
- Adult
- Antigens, CD -- metabolism
- Antigens, Differentiation, Myelomonocytic -- metabolism
- Calbindin 2
- Calbindins
- Case-Control Studies
- Cell Count -- methods
- Child
- Child, Preschool
- Female
- Glial Fibrillary Acidic Protein -- metabolism
- Hippocampus -- cytology
- Humans
- Immunohistochemistry -- methods
- Interneurons -- metabolism
- Lysosomal Storage Diseases -- pathology
- Male
- Microscopy, Confocal -- methods
- Middle Aged
- Nerve Degeneration -- pathology
- Neuroglia -- metabolism
- Neuronal Ceroid-Lipofuscinoses -- classification
- Parvalbumins -- metabolism
- Phenotype
- Postmortem Changes
- S100 Calcium Binding Protein G -- metabolism
- Staining and Labeling -- methods
- Tripeptidyl-Peptidase 1
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Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
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