Defective mitochondrial oxidative phosphorylation in myopathies with tubular aggregates originating from sarcoplasmic reticulum. [electronic resource]
Producer: 20011207Description: 1032-40 p. digitalISSN:- 0022-3069
- Adult
- Biopsy
- Calcium-Transporting ATPases -- analysis
- Calsequestrin -- analysis
- Cell Respiration
- DNA, Mitochondrial -- analysis
- Energy Metabolism
- Humans
- Immunohistochemistry
- Male
- Microscopy, Electron
- Middle Aged
- Mitochondrial Myopathies -- metabolism
- Muscle Fibers, Skeletal -- chemistry
- Muscle, Skeletal -- chemistry
- Oxidative Phosphorylation
- Ryanodine Receptor Calcium Release Channel -- analysis
- Saponins
- Sarcoplasmic Reticulum -- metabolism
- Sarcoplasmic Reticulum Calcium-Transporting ATPases
- Titrimetry
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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